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KO |
09100 Metabolism
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09101 Carbohydrate metabolism
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00010 Glycolysis / Gluconeogenesis [PATH:mpah00010]
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00020 Citrate cycle (TCA cycle) [PATH:mpah00020]
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00030 Pentose phosphate pathway [PATH:mpah00030]
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00040 Pentose and glucuronate interconversions [PATH:mpah00040]
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00051 Fructose and mannose metabolism [PATH:mpah00051]
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00052 Galactose metabolism [PATH:mpah00052]
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00053 Ascorbate and aldarate metabolism [PATH:mpah00053]
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00500 Starch and sucrose metabolism [PATH:mpah00500]
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00520 Amino sugar and nucleotide sugar metabolism [PATH:mpah00520]
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00620 Pyruvate metabolism [PATH:mpah00620]
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00630 Glyoxylate and dicarboxylate metabolism [PATH:mpah00630]
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00640 Propanoate metabolism [PATH:mpah00640]
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110317693 Acss2; acetyl-coenzyme A synthetase, cytoplasmic isoform X1
110318095 Acss1; acetyl-coenzyme A synthetase 2-like, mitochondrial
110326643 Acss3; acyl-CoA synthetase short-chain family member 3, mitochondrial isoform X1
110336437 Bckdha; 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
110327310 Bckdhb; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
110320152 Dbt; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
110324154 Dld; dihydrolipoyl dehydrogenase, mitochondrial isoform X1
110312894 Acads; short-chain specific acyl-CoA dehydrogenase, mitochondrial
110331272 Acox1; peroxisomal acyl-coenzyme A oxidase 1 isoform X1
110330653 Acox3; peroxisomal acyl-coenzyme A oxidase 3
110324206 Hadha; trifunctional enzyme subunit alpha, mitochondrial
110330110 Ehhadh; peroxisomal bifunctional enzyme
110325026 Echs1; enoyl-CoA hydratase, mitochondrial
110322173 Hibch; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
110331113 Acaca; acetyl-CoA carboxylase 1
110312771 Acacb; acetyl-CoA carboxylase 2
110337530 Mlycd; malonyl-CoA decarboxylase, mitochondrial
110329563 Abat; 4-aminobutyrate aminotransferase, mitochondrial isoform X1
110325271 Pcca; propionyl-CoA carboxylase alpha chain, mitochondrial
110327231 Pccb; propionyl-CoA carboxylase beta chain, mitochondrial isoform X1
110338255 Echdc1; ethylmalonyl-CoA decarboxylase isoform X1
110333808 Mcee; methylmalonyl-CoA epimerase, mitochondrial
110335559 Mut; methylmalonyl-CoA mutase, mitochondrial
110316308 Suclg1; succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial
110315980 Suclg2; succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial
110325268 Sucla2; succinate--CoA ligase [ADP-forming] subunit beta, mitochondrial
110324153 Aldh6a1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial isoform X1
110338443 L-lactate dehydrogenase A chain
110315945 Ldhb; L-lactate dehydrogenase B chain isoform X1
110328267 L-lactate dehydrogenase A chain-like
110338173 L-lactate dehydrogenase A-like 6A isoform X1
110326699 L-lactate dehydrogenase A chain isoform X1
110326856 L-lactate dehydrogenase A chain-like isoform X1
110333827 L-lactate dehydrogenase A chain-like isoform X1
|
K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K01908 ACSS3; propionyl-CoA synthetase [EC:6.2.1.17]
K00166 BCKDHA; 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
K00167 BCKDHB; 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
K09699 DBT; 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase) [EC:2.3.1.168]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K11262 ACACA; acetyl-CoA carboxylase / biotin carboxylase 1 [EC:6.4.1.2 6.3.4.14 2.1.3.15]
K01946 ACACB; acetyl-CoA carboxylase / biotin carboxylase 2 [EC:6.4.1.2 6.3.4.14 2.1.3.15]
K01578 MLYCD; malonyl-CoA decarboxylase [EC:4.1.1.9]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K01965 PCCA; propionyl-CoA carboxylase alpha chain [EC:6.4.1.3]
K01966 PCCB; propionyl-CoA carboxylase beta chain [EC:6.4.1.3 2.1.3.15]
K18426 ECHDC1; ethylmalonyl-CoA/methylmalonyl-CoA decarboxylase [EC:4.1.1.94 4.1.1.-]
K05606 MCEE; methylmalonyl-CoA/ethylmalonyl-CoA epimerase [EC:5.1.99.1]
K01847 MUT; methylmalonyl-CoA mutase [EC:5.4.99.2]
K01899 LSC1; succinyl-CoA synthetase alpha subunit [EC:6.2.1.4 6.2.1.5]
K01900 LSC2; succinyl-CoA synthetase beta subunit [EC:6.2.1.4 6.2.1.5]
K01900 LSC2; succinyl-CoA synthetase beta subunit [EC:6.2.1.4 6.2.1.5]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
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00650 Butanoate metabolism [PATH:mpah00650]
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110338406 acetyl-CoA acetyltransferase, cytosolic
110338461 acetyl-CoA acetyltransferase, cytosolic-like
110327655 Acat1; acetyl-CoA acetyltransferase, mitochondrial
110320141 Hadh; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial isoform X1
110324206 Hadha; trifunctional enzyme subunit alpha, mitochondrial
110330110 Ehhadh; peroxisomal bifunctional enzyme
110325026 Echs1; enoyl-CoA hydratase, mitochondrial
110312894 Acads; short-chain specific acyl-CoA dehydrogenase, mitochondrial
110326344 Acsm1; acyl-coenzyme A synthetase ACSM1, mitochondrial
110325118 Acsm2b; acyl-coenzyme A synthetase ACSM2B, mitochondrial
110323274 Acsm5; acyl-coenzyme A synthetase ACSM5, mitochondrial isoform X1
110324507 Acsm4; acyl-coenzyme A synthetase ACSM4, mitochondrial
110316032 Acsm3; acyl-coenzyme A synthetase ACSM3, mitochondrial
110324754 L2hgdh; L-2-hydroxyglutarate dehydrogenase, mitochondrial
110326820 glutamate decarboxylase 1
110317896 glutamate decarboxylase 1-like
110318146 Gad2; glutamate decarboxylase 2
110329563 Abat; 4-aminobutyrate aminotransferase, mitochondrial isoform X1
110333905 Aldh5a1; succinate-semialdehyde dehydrogenase, mitochondrial
110320299 Hmgcs2; hydroxymethylglutaryl-CoA synthase, mitochondrial isoform X1
110328741 Hmgcs1; hydroxymethylglutaryl-CoA synthase, cytoplasmic isoform X1
110323291 Hmgcl; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1
110327857 Hmgcll1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic
110328779 Oxct1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial isoform X1
110322868 Oxct2; succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial
110339181 Aacs; acetoacetyl-CoA synthetase isoform X1
110329658 Bdh1; D-beta-hydroxybutyrate dehydrogenase, mitochondrial
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K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K23756 ACSM1; medium-chain acyl-CoA ligase / lipoate-activating enzyme [EC:6.2.1.2]
K01896 ACSM; medium-chain acyl-CoA synthetase [EC:6.2.1.2]
K01896 ACSM; medium-chain acyl-CoA synthetase [EC:6.2.1.2]
K01896 ACSM; medium-chain acyl-CoA synthetase [EC:6.2.1.2]
K01896 ACSM; medium-chain acyl-CoA synthetase [EC:6.2.1.2]
K00109 L2HGDH; 2-hydroxyglutarate dehydrogenase [EC:1.1.99.2]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K00139 ALDH5A1; succinate-semialdehyde dehydrogenase [EC:1.2.1.24]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01907 AACS; acetoacetyl-CoA synthetase [EC:6.2.1.16]
K00019 BDH1; 3-hydroxybutyrate dehydrogenase [EC:1.1.1.30]
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00660 C5-Branched dibasic acid metabolism
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00562 Inositol phosphate metabolism [PATH:mpah00562]
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09102 Energy metabolism
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09103 Lipid metabolism
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00061 Fatty acid biosynthesis [PATH:mpah00061]
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00062 Fatty acid elongation [PATH:mpah00062]
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00071 Fatty acid degradation [PATH:mpah00071]
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110338406 acetyl-CoA acetyltransferase, cytosolic
110338461 acetyl-CoA acetyltransferase, cytosolic-like
110327655 Acat1; acetyl-CoA acetyltransferase, mitochondrial
110328451 3-ketoacyl-CoA thiolase A, peroxisomal-like
110327492 Acaa1; 3-ketoacyl-CoA thiolase, peroxisomal isoform X1
110333199 Acaa2; 3-ketoacyl-CoA thiolase, mitochondrial
110324296 Hadhb; trifunctional enzyme subunit beta, mitochondrial isoform X1
110320141 Hadh; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial isoform X1
110324206 Hadha; trifunctional enzyme subunit alpha, mitochondrial
110330110 Ehhadh; peroxisomal bifunctional enzyme
110325026 Echs1; enoyl-CoA hydratase, mitochondrial
110331272 Acox1; peroxisomal acyl-coenzyme A oxidase 1 isoform X1
110330653 Acox3; peroxisomal acyl-coenzyme A oxidase 3
110312894 Acads; short-chain specific acyl-CoA dehydrogenase, mitochondrial
110320920 Acadm; medium-chain specific acyl-CoA dehydrogenase, mitochondrial
110321743 Acadl; long-chain specific acyl-CoA dehydrogenase, mitochondrial
110326470 Acadsb; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
110332221 Acadvl; very long-chain specific acyl-CoA dehydrogenase, mitochondrial isoform X1
110337330 Gcdh; glutaryl-CoA dehydrogenase, mitochondrial
110313469 Acsl4; long-chain-fatty-acid--CoA ligase 4 isoform X1
110321273 Acsl3; long-chain-fatty-acid--CoA ligase 3
110332134 Acsl6; long-chain-fatty-acid--CoA ligase 6 isoform X1
110317632 Acsl5; long-chain-fatty-acid--CoA ligase 5 isoform X1
110336203 Acsl1; long-chain-fatty-acid--CoA ligase 1
110327969 Acsbg1; long-chain-fatty-acid--CoA ligase ACSBG1
110335950 long-chain-fatty-acid--CoA ligase ACSBG2-like
110335987 Acsbg2; long-chain-fatty-acid--CoA ligase ACSBG2
110338994 Cpt1a; carnitine O-palmitoyltransferase 1, liver isoform
110334540 Cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform
110319999 Cpt1c; carnitine O-palmitoyltransferase 1, brain isoform isoform X1
110323321 Cpt2; carnitine O-palmitoyltransferase 2, mitochondrial isoform X1
110338318 Eci1; enoyl-CoA delta isomerase 1, mitochondrial
110333815 enoyl-CoA delta isomerase 2, mitochondrial isoform X1
110333969 enoyl-CoA delta isomerase 3, peroxisomal isoform X1
110320955 cytochrome P450 2U1 isoform X1
110323152 LOW QUALITY PROTEIN: cytochrome P450 4A10-like
110315778 cytochrome P450 4A12A isoform X1
110323837 cytochrome P450 4A10-like
110322859 cytochrome P450 4A14 isoform X1
110322974 cytochrome P450 4A10-like isoform X1
110320167 alcohol dehydrogenase 1
110320307 Adh7; alcohol dehydrogenase class 4 mu/sigma chain
110320387 Adh4; alcohol dehydrogenase 4
110319844 alcohol dehydrogenase class-3 isoform X1
110313054 Aldh2; aldehyde dehydrogenase, mitochondrial isoform X1
110323147 Aldh1b1; aldehyde dehydrogenase X, mitochondrial
110331656 fatty aldehyde dehydrogenase isoform X1
110333007 Aldh7a1; alpha-aminoadipic semialdehyde dehydrogenase isoform X1
110321543 Aldh9a1; 4-trimethylaminobutyraldehyde dehydrogenase
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K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K00255 ACADL; long-chain-acyl-CoA dehydrogenase [EC:1.3.8.8]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K09479 ACADVL; very long chain acyl-CoA dehydrogenase [EC:1.3.8.9]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K15013 ACSBG; long-chain-fatty-acid--CoA ligase ACSBG [EC:6.2.1.3]
K15013 ACSBG; long-chain-fatty-acid--CoA ligase ACSBG [EC:6.2.1.3]
K15013 ACSBG; long-chain-fatty-acid--CoA ligase ACSBG [EC:6.2.1.3]
K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
K08766 CPT2; carnitine O-palmitoyltransferase 2 [EC:2.3.1.21]
K13238 ECI1; Delta3-Delta2-enoyl-CoA isomerase [EC:5.3.3.8]
K13239 ECI2; Delta3-Delta2-enoyl-CoA isomerase [EC:5.3.3.8]
K13239 ECI2; Delta3-Delta2-enoyl-CoA isomerase [EC:5.3.3.8]
K07422 CYP2U1; long-chain fatty acid omega-monooxygenase [EC:1.14.14.80]
K07425 CYP4A; long-chain fatty acid omega-monooxygenase [EC:1.14.14.80]
K07425 CYP4A; long-chain fatty acid omega-monooxygenase [EC:1.14.14.80]
K07425 CYP4A; long-chain fatty acid omega-monooxygenase [EC:1.14.14.80]
K07425 CYP4A; long-chain fatty acid omega-monooxygenase [EC:1.14.14.80]
K07425 CYP4A; long-chain fatty acid omega-monooxygenase [EC:1.14.14.80]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13980 ADH4; alcohol dehydrogenase 4 [EC:1.1.1.1]
K00121 frmA; S-(hydroxymethyl)glutathione dehydrogenase / alcohol dehydrogenase [EC:1.1.1.284 1.1.1.1]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
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00073 Cutin, suberine and wax biosynthesis
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00100 Steroid biosynthesis [PATH:mpah00100]
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00120 Primary bile acid biosynthesis [PATH:mpah00120]
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00121 Secondary bile acid biosynthesis
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00140 Steroid hormone biosynthesis [PATH:mpah00140]
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00561 Glycerolipid metabolism [PATH:mpah00561]
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00564 Glycerophospholipid metabolism [PATH:mpah00564]
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00565 Ether lipid metabolism [PATH:mpah00565]
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00600 Sphingolipid metabolism [PATH:mpah00600]
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00590 Arachidonic acid metabolism [PATH:mpah00590]
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00591 Linoleic acid metabolism [PATH:mpah00591]
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00592 alpha-Linolenic acid metabolism [PATH:mpah00592]
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01040 Biosynthesis of unsaturated fatty acids [PATH:mpah01040]
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09104 Nucleotide metabolism
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09105 Amino acid metabolism
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00250 Alanine, aspartate and glutamate metabolism [PATH:mpah00250]
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00260 Glycine, serine and threonine metabolism [PATH:mpah00260]
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00270 Cysteine and methionine metabolism [PATH:mpah00270]
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00280 Valine, leucine and isoleucine degradation [PATH:mpah00280]
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110316419 Bcat1; branched-chain-amino-acid aminotransferase, cytosolic isoform X1
110321294 Bcat2; branched-chain-amino-acid aminotransferase, mitochondrial isoform X1
110323726 L-amino-acid oxidase-like
110331259 L-amino-acid oxidase-like
110324379 Il4i1; L-amino-acid oxidase isoform X1
110336437 Bckdha; 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
110327310 Bckdhb; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
110320152 Dbt; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
110324154 Dld; dihydrolipoyl dehydrogenase, mitochondrial isoform X1
110312894 Acads; short-chain specific acyl-CoA dehydrogenase, mitochondrial
110320920 Acadm; medium-chain specific acyl-CoA dehydrogenase, mitochondrial
110318371 Ivd; isovaleryl-CoA dehydrogenase, mitochondrial
110326470 Acadsb; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
110327771 Acad8; isobutyryl-CoA dehydrogenase, mitochondrial
110324206 Hadha; trifunctional enzyme subunit alpha, mitochondrial
110330110 Ehhadh; peroxisomal bifunctional enzyme
110325026 Echs1; enoyl-CoA hydratase, mitochondrial
110320141 Hadh; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial isoform X1
110313838 Hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 isoform X1
110328451 3-ketoacyl-CoA thiolase A, peroxisomal-like
110327492 Acaa1; 3-ketoacyl-CoA thiolase, peroxisomal isoform X1
110333199 Acaa2; 3-ketoacyl-CoA thiolase, mitochondrial
110324296 Hadhb; trifunctional enzyme subunit beta, mitochondrial isoform X1
110325271 Pcca; propionyl-CoA carboxylase alpha chain, mitochondrial
110327231 Pccb; propionyl-CoA carboxylase beta chain, mitochondrial isoform X1
110333808 Mcee; methylmalonyl-CoA epimerase, mitochondrial
110335559 Mut; methylmalonyl-CoA mutase, mitochondrial
110322173 Hibch; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
110316426 Hibadh; 3-hydroxyisobutyrate dehydrogenase, mitochondrial
110324153 Aldh6a1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial isoform X1
110313054 Aldh2; aldehyde dehydrogenase, mitochondrial isoform X1
110323147 Aldh1b1; aldehyde dehydrogenase X, mitochondrial
110331656 fatty aldehyde dehydrogenase isoform X1
110333007 Aldh7a1; alpha-aminoadipic semialdehyde dehydrogenase isoform X1
110321543 Aldh9a1; 4-trimethylaminobutyraldehyde dehydrogenase
110321275 aldehyde oxidase 3 isoform X1
110321290 Aox1; aldehyde oxidase
110321921 aldehyde oxidase 4
110337582 Acsf3; acyl-CoA synthetase family member 3, mitochondrial
110329563 Abat; 4-aminobutyrate aminotransferase, mitochondrial isoform X1
110328982 Agxt2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1
110328965 Mccc2; methylcrotonoyl-CoA carboxylase beta chain, mitochondrial
110333897 Auh; methylglutaconyl-CoA hydratase, mitochondrial isoform X1
110323291 Hmgcl; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1
110327857 Hmgcll1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic
110328779 Oxct1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial isoform X1
110322868 Oxct2; succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial
110339181 Aacs; acetoacetyl-CoA synthetase isoform X1
110338406 acetyl-CoA acetyltransferase, cytosolic
110338461 acetyl-CoA acetyltransferase, cytosolic-like
110327655 Acat1; acetyl-CoA acetyltransferase, mitochondrial
110320299 Hmgcs2; hydroxymethylglutaryl-CoA synthase, mitochondrial isoform X1
110328741 Hmgcs1; hydroxymethylglutaryl-CoA synthase, cytoplasmic isoform X1
|
K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K03334 IL4I1; L-amino-acid oxidase [EC:1.4.3.2]
K03334 IL4I1; L-amino-acid oxidase [EC:1.4.3.2]
K03334 IL4I1; L-amino-acid oxidase [EC:1.4.3.2]
K00166 BCKDHA; 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
K00167 BCKDHB; 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
K09699 DBT; 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase) [EC:2.3.1.168]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K00253 IVD; isovaleryl-CoA dehydrogenase [EC:1.3.8.4]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K11538 ACAD8; isobutyryl-CoA dehydrogenase [EC:1.3.99.-]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K01965 PCCA; propionyl-CoA carboxylase alpha chain [EC:6.4.1.3]
K01966 PCCB; propionyl-CoA carboxylase beta chain [EC:6.4.1.3 2.1.3.15]
K05606 MCEE; methylmalonyl-CoA/ethylmalonyl-CoA epimerase [EC:5.1.99.1]
K01847 MUT; methylmalonyl-CoA mutase [EC:5.4.99.2]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K00020 HIBADH; 3-hydroxyisobutyrate dehydrogenase [EC:1.1.1.31]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
K00157 AOX; aldehyde oxidase [EC:1.2.3.1]
K00157 AOX; aldehyde oxidase [EC:1.2.3.1]
K00157 AOX; aldehyde oxidase [EC:1.2.3.1]
K18660 ACSF3; malonyl-CoA/methylmalonyl-CoA synthetase [EC:6.2.1.76 6.2.1.-]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K00827 AGXT2; alanine-glyoxylate transaminase / (R)-3-amino-2-methylpropionate-pyruvate transaminase [EC:2.6.1.44 2.6.1.40]
K01969 MCCC2; 3-methylcrotonyl-CoA carboxylase beta subunit [EC:6.4.1.4]
K05607 AUH; methylglutaconyl-CoA hydratase [EC:4.2.1.18]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01907 AACS; acetoacetyl-CoA synthetase [EC:6.2.1.16]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
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00290 Valine, leucine and isoleucine biosynthesis [PATH:mpah00290]
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00300 Lysine biosynthesis
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00310 Lysine degradation [PATH:mpah00310]
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00220 Arginine biosynthesis [PATH:mpah00220]
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00330 Arginine and proline metabolism [PATH:mpah00330]
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00340 Histidine metabolism [PATH:mpah00340]
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00350 Tyrosine metabolism [PATH:mpah00350]
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00360 Phenylalanine metabolism [PATH:mpah00360]
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00380 Tryptophan metabolism [PATH:mpah00380]
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00400 Phenylalanine, tyrosine and tryptophan biosynthesis [PATH:mpah00400]
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09106 Metabolism of other amino acids
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00410 beta-Alanine metabolism [PATH:mpah00410]
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110334767 Csad; cysteine sulfinic acid decarboxylase
110328115 Gadl1; acidic amino acid decarboxylase GADL1
110326820 glutamate decarboxylase 1
110317896 glutamate decarboxylase 1-like
110318146 Gad2; glutamate decarboxylase 2
110333472 Cndp1; beta-Ala-His dipeptidase
110336527 Carns1; carnosine synthase 1
110332928 Cndp2; cytosolic non-specific dipeptidase
110329563 Abat; 4-aminobutyrate aminotransferase, mitochondrial isoform X1
110317651 Smox; spermine oxidase isoform X1
110332162 Aoc2; retina-specific copper amine oxidase
110332463 Aoc3; membrane primary amine oxidase
110313054 Aldh2; aldehyde dehydrogenase, mitochondrial isoform X1
110323147 Aldh1b1; aldehyde dehydrogenase X, mitochondrial
110331656 fatty aldehyde dehydrogenase isoform X1
110333007 Aldh7a1; alpha-aminoadipic semialdehyde dehydrogenase isoform X1
110321543 Aldh9a1; 4-trimethylaminobutyraldehyde dehydrogenase
110331990 Aldh3a1; aldehyde dehydrogenase, dimeric NADP-preferring isoform X1
110327470 aldehyde dehydrogenase family 3 member B1
110325520 aldehyde dehydrogenase family 3 member B2 isoform X1
110320876 Dpyd; dihydropyrimidine dehydrogenase [NADP(+)]
110334818 Dpys; dihydropyrimidinase
110326870 Upb1; beta-ureidopropionase
110322173 Hibch; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
110324206 Hadha; trifunctional enzyme subunit alpha, mitochondrial
110330110 Ehhadh; peroxisomal bifunctional enzyme
110325026 Echs1; enoyl-CoA hydratase, mitochondrial
110312894 Acads; short-chain specific acyl-CoA dehydrogenase, mitochondrial
110331272 Acox1; peroxisomal acyl-coenzyme A oxidase 1 isoform X1
110330653 Acox3; peroxisomal acyl-coenzyme A oxidase 3
110337530 Mlycd; malonyl-CoA decarboxylase, mitochondrial
110324153 Aldh6a1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial isoform X1
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K18966 GADL1; sulfinoalanine decarboxylase / aspartate 1-decarboxylase [EC:4.1.1.29 4.1.1.11]
K18966 GADL1; sulfinoalanine decarboxylase / aspartate 1-decarboxylase [EC:4.1.1.29 4.1.1.11]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K05604 CNDP1; beta-Ala-His dipeptidase [EC:3.4.13.20]
K14755 CRNS1; carnosine synthase [EC:6.3.2.11]
K08660 CNDP2; cytosolic nonspecific dipeptidase [EC:3.4.13.18]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K12259 SMOX; spermine oxidase [EC:1.5.3.16 1.5.3.-]
K00276 AOC3; primary-amine oxidase [EC:1.4.3.21]
K00276 AOC3; primary-amine oxidase [EC:1.4.3.21]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
K00129 ALDH3; aldehyde dehydrogenase (NAD(P)+) [EC:1.2.1.5]
K00129 ALDH3; aldehyde dehydrogenase (NAD(P)+) [EC:1.2.1.5]
K00129 ALDH3; aldehyde dehydrogenase (NAD(P)+) [EC:1.2.1.5]
K00207 DPYD; dihydropyrimidine dehydrogenase (NADP+) [EC:1.3.1.2]
K01464 DPYS; dihydropyrimidinase [EC:3.5.2.2]
K01431 UPB1; beta-ureidopropionase [EC:3.5.1.6]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K01578 MLYCD; malonyl-CoA decarboxylase [EC:4.1.1.9]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
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00430 Taurine and hypotaurine metabolism [PATH:mpah00430]
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00440 Phosphonate and phosphinate metabolism [PATH:mpah00440]
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00450 Selenocompound metabolism [PATH:mpah00450]
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00460 Cyanoamino acid metabolism
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00470 D-Amino acid metabolism [PATH:mpah00470]
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00480 Glutathione metabolism [PATH:mpah00480]
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09107 Glycan biosynthesis and metabolism
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09108 Metabolism of cofactors and vitamins
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09109 Metabolism of terpenoids and polyketides
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09110 Biosynthesis of other secondary metabolites
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09111 Xenobiotics biodegradation and metabolism
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09112 Not included in regular maps
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09120 Genetic Information Processing
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09130 Environmental Information Processing
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09140 Cellular Processes
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09150 Organismal Systems
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09160 Human Diseases
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09180 Brite Hierarchies
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09190 Not Included in Pathway or Brite
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